Which condition is characterized by the presence of heart myxomas and tumors in endocrine tissues?

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The condition characterized by the presence of heart myxomas and tumors in endocrine tissues is Carney complex. This genetic syndrome is associated with multiple types of tumors, including cardiac myxomas, which are benign tumors that typically occur in the heart. In addition to myxomas, individuals with Carney complex may also develop other types of neoplasms, such as endocrine tumors, particularly in the adrenal glands and the pituitary gland.

The presence of these diverse tumors is a key feature of Carney complex, and it distinguishes this condition from other genetic syndromes. For example, Birt Hogg Dube Syndrome is primarily linked with skin lesions, renal tumors, and lung cysts. CMMRD (Constitutional Mismatch Repair Deficiency) involves an increased risk for various cancers, particularly certain types of childhood cancers, but does not typically present with heart myxomas or endocrine tumors. Familial atypical multiple mole melanoma syndrome is closely associated with melanoma and atypical nevi but does not encompass the cardiac and endocrine manifestations seen in Carney complex.

Overall, the distinct association of cardiac myxomas and endocrine tumors in Carney complex is what makes it the correct answer to this question.

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