What condition is described by malformation of the tricuspid valve with atrialization of the right ventricle?

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The condition characterized by malformation of the tricuspid valve leading to atrialization of the right ventricle is Ebstein anomaly. In this congenital heart defect, the tricuspid valve is abnormally positioned and malformed, allowing blood to flow inefficiently from the right atrium to the right ventricle. As a result, the right ventricle becomes partially atrialized, meaning that a part of it functions more like an atrium rather than a ventricle.

Ebstein anomaly is associated with various cardiovascular complications, including arrhythmias and heart failure, due to the heart’s improper structure and function. The distinct feature of atrialization of the right ventricle is what sets this condition apart from other cardiac anomalies.

In contrast, the other conditions listed do not involve the specific malformation of the tricuspid valve or the atrialization of the right ventricle. Hypertelorism is a facial feature characterized by widely spaced eyes, Potter sequence refers to a group of physical deformities resulting from oligohydramnios, and cleft lip and palate are congenital deformities resulting from the improper fusion of the facial processes. Therefore, these options do not match the description provided in the question.

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